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Adult Congenital Heart Disease: A Practical Guide



Adult Congenital Heart Disease: A Practical Guide


Congenital heart disease with its worldwide incidence of 1% is the most common inborn defect. Increasingly, patients are living into adulthood, with ongoing congenital heart and other medical needs. Sadly, only a small minority have specialist follow-up. However, all patients see their family doctor and may also seek advice from other health professionals.

This practical guide with its straightforward a,b,c approach is written for those professionals.

Special features of this book:

• Introduces the principles of congenital heart disease and tells you whom and when to refer for specialist care
• Discusses common congenital heart lesions in a practical, easy-to-follow way, with an emphasis on diagnosis and management issues
• Includes an extensive chapter on 'Pregnancy and Contraception' (by Philip J. Steer), essential both for family planning and for managing safely the pregnant woman with congenital heart disease
• Includes chapters on non-cardiac surgery and lifestyle issues such as work, insurability, travel and driving
• Provides invaluable information on dealing with common emergencies; what to do and what not to do

With a wealth of illustrations (including diagrams, EKGs, CXRs, Echos and cardiac MRIs) and with key point tables, this is an essential guide for all health care professionals managing patients with adult congenital heart disease.

Foreword vii

Preface ix

Acknowledgments x

Part 1 General Principles 1

1 Epidemiology of Congenital Heart Disease 3

2 Services for the Adult with Congenital Heart Disease 8

3 Pregnancy and Contraception 16

4 Infective Endocarditis Prophylaxis 36

5 Anticoagulation 42

6 Lifestyle Issues 49

7 Long-Term Outcome 60

Part 2 Common Lesions 65

8 Atrial Septal Defects and Anomalous Pulmonary Venous Drainage 67

9 Ventricular Septal Defect 82

10 Atrioventricular Septal Defect 87

11 Left Ventricular Outfl ow Tract Disorders 92

12 Coarctation of the Aorta 97

13 Complete Transposition of the Great Arteries 103

14 The Single Ventricle and Fontan Circulations 112

15 Tetralogy of Fallot and Right Ventricular Outfl ow Tract Disorders 125

16 Pulmonary Atresia with Ventricular Septal Defect 132

17 Ebstein’s Anomaly of the Tricuspid Valve 139

18 Patent Arterial Duct 145

19 Marfan Syndrome 153

20 Eisenmenger Syndrome 161

21 Other Lesions 174

22 Pulmonary Hypertension 182

Part 3 Emergencies and Special Situations 189

23 Arrhythmia and Syncope 191

24 Suspected Infective Endocarditis 196

25 Perioperative Care 201

26 Heart Failure: Acute Management 206

27 Care of the Cyanosed Patient 209

Bibliography 213

Glossary 217

Appendix: Shunt Calculations 257

Index 261

"an easy to read manual of adult congenital heart disease...the authors provide easy to understand diagrams, echocardiograms, electrocardiograms, and chest x-rays. The illustrations are excellent...This will be a very useful book for practitioners caring for adults with congenital heart disease."

Rishi G Anand, MD (Ochsner Clinic Foundation) - Doody's

"This book is a useful guide...clearly laid out, well illustrated and is written in an authoritative style. Gatzoulis and colleagues' book is a welcome addition to this speciality"

Richard Hatchett - British Journal of Cardiac Nursing, May 2006

An essential guide to managing adult survivors of congenital heart disease

  • A practical book intended for the non-specialist
  • Concise clinical text backed up with outstanding colour illustrations
  • Covers important lifestyle issues that patients frequently ask about
  • Written by leading specialists from North America and the UK