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Hypoplastic Left Heart Syndrome

Hypoplastic Left Heart Syndrome

Hani A. Hennein M. D. FACS (Editor), Edward L. Bove M. D. (Editor)

ISBN: 978-0-879-93704-1

Aug 2002, Wiley-Blackwell

352 pages

Select type: Hardcover

Out of stock



The sucessful treatment of hypoplastic left heart syndrome (HLHS) is the culmination of five decades of experience in the treatment of congenital heart disease. This text, the first to devoted solely to the implications and treatment of this single congenital heart malformation, takes a comprehensive look at the medical and surgical therapy for hypoplastic left heart syndrome.

Starting from the salient genetics invoved, contributors proceed to cover to the impact of fetal echocardiography, staged palliation, cardiac transplantation, long-term outlooks, and the treatment of advanced disease. Additionally, this essential text explores the difficult topic of HLHS variants, and the perspective of the parent whose child has HLHS.


William Norwood, MD.


Chapter 1. Morphology of the Hypoplastic Left Heart Syndrome and Variants, and Causes of Death Following the Modified Norwood and Fontan Procedures.

Richard Van Praagh, MD, Ulrike Bartram, MD, and Maria Kiaffas, MD.

Chapter 2. Hypoplastic Left Heart Syndrome: Incidence, Epidemiology, and Ethics.

Elizabeth A. Fisher, MD, FACC.

Chapter 3. The Genetics of Hypoplastic Left Heart Syndrome.

Paul Grossfeld, MD.

Chapter 4. Hypoplastic Left Heart Syndrome in the Fetus: The Role of Fetal Echocardiography in Prenatal Diagnosis, Management, and Outcome.

Benjamin W. Eidem, MD.

Chapter 5. Clinical Presentation and Noninvasive Assessment of the Infant with Hypoplastic Left Heart Syndrome.

Benjamin W. Eidem, MD and Dolores A. Vitullo, MD.

Chapter 6. Anesthetic Considerations for Patients with Hypoplastic Left Heart Syndrome for Staged Reconstructive Surgery.

Susan Craig Nicolson, MD, James M. Steven, MD, and David R. Jobes, MD.

Chapter 7. Cardiopulmonary Bypass and Extracorporeal Support for Infants Undergoing Repair of Hypoplastic Left Heart Syndrome.

Dale M. Geiss, MD, Gary W. Raff, MD, Melinda S. Dickes, CCP, and Klayton W. Buckley, CCP.

Chapter 8. Physiology of Staged Palliation.

Hani A. Hennein, MD.

Chapter 9. Staged Reconstruction for Hypoplastic Left Heart Syndrome: The Norwood Operation.

Edward L. Bove, MD.

Chapter 10. Staged Reconstruction for Hypoplastic Left Heart Syndrome: The Cavopulmonary Anastomosis.

Joseph J. Amato, MD, William I. Douglas, MD, and Uptal Desai, MD.

Chapter 11. The Fontan Operation for Hypoplastic Left Heart Syndrome.

Hani A. Hennein, MD, FACS.

Chapter 12. Hypoplastic Left Heart Syndrome Variants.

Hani A. Hennein, MD, FACS.

Chapter 13. Intensive Care of Infants and Children with Hypoplastic Left Heart Syndrome.

Steven M. Schwartz, MD, David P. Nelson, MD, PhD, and Roozbeh Taeed, MD.

Chapter 14. Postoperative Management of Patients Following the Norwood Prodcedure for Hypoplastic Left Heart Syndrome Using Phenoxybenzamine.

James S. Tweddell, MD and George M. Hoffman, MD.

Chapter 15. Diagnosis and Management of Late Atrial Arrhythmias following Fontan Surgery.

Barbara J. Deal, MD, Constantine Mavroudis, MD, Carl Backer, MD and Christopher Johnsrude, MD.

Chapter 16. The Fontan Operation in the 2000s: Lessons Learned.

Frank Cetta, MD and David J. Driscoll, MD.

Chapter 17. Hypoplastic Left Heart Syndrome: Surgical Treatment of Advanced Disease.

Carl L. Backer, MD, Constantine Mavroudis, MD, and Barbara J. Deal, MD.

Chapter 18. Transplantation for Hypoplastic Left Heart Syndrome.

Timothy M. Hoffman, MD and Thomas L. Spray, MD.

Chapter 19. Induction of Left Ventricular Growth to Achieve Two Ventricle Repairs in HLHS Subsets.

John E. Foker, MD, James Berry, MD, Julia Steinberger, MD.

Chapter 20. Hypoplastic Left Heart Syndrome: A Parent's Perspective.

Anna Jaworski, MEd.

  • Includes comprehensive information on the medical and surgical therapy for HLHS

  • Introduces the parent's perspective of having a child with HLHS

  • Examines HLHS variants, offering insight into occasions for single-ventricle palliation or a biventrivular repair